Porokeratotic eccrine and hair follicle nevus: a report of two cases and review of the literature*
نویسندگان
چکیده
Porokeratotic eccrine and hair follicle nevus is a very rare non-hereditary disorder of keratinization with eccrine and hair follicle involvement with only 9 cases described in the literature. In 2009 the term porokeratotic anexial ostial nevus was proposed to comprehend porokeratotic eccrine and hair follicle nevus and a related and more common process without follicular involvement: porokeratotic eccrine ostial and dermal duct nevus Recent findings suggest that both entities may be produced by a mutation in GJB2 gene, which is associated to KID syndrome. Herein we report 2 cases of porokeratotic eccrine and hair follicle nevus and review the existing cases in the Spanish and English literature.
منابع مشابه
Porokeratotic eccrine ostial and dermal duct nevus (PEODDN): A case report
Porokeratotic Eccrine Ostial and Dermal Duct Nevus (PEODDN) is a rare disorder of keratinization that clinically resembles comedo nevus but occurs on the palms and soles and is characterized by cornoid lamella in the histopathology. We hereunder report a young male with mildly itchy papules on the lateral surface of the left foot who was diagnosed with PEODDN upon biopsy of the lesion. We brief...
متن کاملPorokeratotic eccrine ostial and dermal duct nevus with sensory polyneuropathy and hyperthyroidism: Report of a case
The case, who discribed here is a 66-year-old man with one year history of asymptomatic, keratotic papules with a linear distribution on the skin of his right palm near the wrist. On histopathological examination cornoid lamella-like parakeratotic columns above eccrine sweat ducts were observed. The acrosyringium was also dilated. He had been followed up for predominantly sensory polyneur...
متن کاملPorokeratotic Eccrine Ostial and Dermal Duct Nevus
Comedo-like lesions of the palm, present since birth, are studied electronmicroscopically and their eccrine nature demonstrated. We suggest their inclusion under the name porokeratotic eccrine-ostial and dermal duct nevus previously proposed by Abell and Read.
متن کاملPorokeratotic eccrine ostial and dermal duct nevus with extensive linear distribution: a case report
Porokeratotic eccrine ostial and dermal duct nevus (PEODDN) is known as an uncommon disorder of keratinization in which acrosyringium is involved; however, its causes have yet remained unknown. It is presented clinically by discrete keratotic papules on distal extremities arranged in a linear pattern along Blaschko lines. Histopathologically, it is characterized by cornoid lamella, which is alm...
متن کامل[Hair follicle nevus: a case report and review of the literature].
The study of hair follicle tumors can be confusing, and hair follicle nevi are no exception. Analogous lesions frequently have divergent appellations. We evaluated the English-language literature on hair follicle nevi and histologic equivalents from 1921 to 1994. In addition, we reviewed four standard dermatopathology textbooks for further examples. We found 20 published valid cases of hair fol...
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